Both Hemophilia Health Care Providers and Hemophilia A Carriers Report That Carriers Have Excessive Bleeding
| Autor: | Michael R. DeBaun, Allison Paroskie, Benjamin Almassi, Robert F. Sidonio, Olatunde Oso |
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| Rok vydání: | 2014 |
| Předmět: |
Adult
Male Excessive Bleeding Heterozygote congenital hereditary and neonatal diseases and abnormalities medicine.medical_specialty Pediatrics Cross-sectional study Health Personnel Hemorrhage Carrier testing Hemophilia A Article Surveys and Questionnaires hemic and lymphatic diseases Health care medicine Humans Prospective cohort study Factor VIII business.industry Data Collection Hematology Factor VIII Activity Middle Aged Clinical trial Cross-Sectional Studies Oncology Pediatrics Perinatology and Child Health Physical therapy Carrier status Female business |
| Zdroj: | Journal of Pediatric Hematology/Oncology. 36:e224-e230 |
| ISSN: | 1077-4114 |
| DOI: | 10.1097/mph.0000000000000022 |
| Popis: | INTRODUCTION Hemophilia A, the result of reduced factor VIII activity, is an X-linked recessive bleeding disorder. Previous reports of hemophilia A carriers suggest an increased bleeding tendency. Our objective was to determine the attitudes and understanding of the hemophilia A carrier bleeding phenotype, and opinions regarding timing of carrier testing from the perspective of both medical providers and affected patients. Data from this survey were used as preliminary data for an ongoing prospective study. MATERIALS AND METHODS An electronic survey was distributed to physicians and nurses employed at Hemophilia Treatment Centers, and hemophilia A carriers who were members of Hemophilia Federation of America. The questions focused on the clinical understanding of bleeding symptoms and management of hemophilia A carriers, and the timing and intensity of carrier testing. RESULTS Our survey indicates that 51% (36/51) of providers compared with 78% (36/46) of carriers believe that hemophilia A carriers with normal factor VIII activity have an increased bleeding tendency (P |
| Databáze: | OpenAIRE |
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