Tracheobronchial Amyloidosis in a Patient With Sjogren Syndrome
| Autor: | Erik Folch, Adnan Majid, Hanine Inaty, Christopher D. Stephen |
|---|---|
| Rok vydání: | 2013 |
| Předmět: |
Lung Diseases
Male Pulmonary and Respiratory Medicine Pathology medicine.medical_specialty Pulmonary amyloidosis Sjögren syndrome Laser therapy Bronchoscopy Submucosa medicine Humans Tracheal Diseases medicine.diagnostic_test business.industry Bronchial Diseases Amyloidosis Middle Aged respiratory system medicine.disease Sjogren's Syndrome medicine.anatomical_structure Debridement Tracheobronchial amyloidosis Airway business |
| Zdroj: | Journal of Bronchology & Interventional Pulmonology. 20:261-265 |
| ISSN: | 1944-6586 |
| Popis: | Pulmonary amyloidosis in the setting of Sjogren syndrome is rare. It most commonly presents in form of multinodular disease with or without cysts formation. Amyloid plaques may also deposit in the airway submucosa, causing airway narrowing; the condition referred as "tracheobronchial amyloidosis" (TBA). Patients with this condition most commonly present with postobstructive pneumonia, wheezing, and occasionally hemoptysis. Endoscopic therapies, using flexible forceps with or without laser therapy is crucial to alleviate the obstruction and control the bleeding. Other therapeutic modalities such as external beam radiation has been shown to be promising; however, further data are still needed. To our knowledge, our patient is the first reported case of TBA in a setting of Sjogren syndrome. |
| Databáze: | OpenAIRE |
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