The outcome of Jarcho-Levin syndrome treated with a functional latissimus dorsi flap - A series of three cases
| Autor: | Rujuta Mehta, Mukund R Thatte, Bipin A Gangurde, Binita Bharat Raut |
|---|---|
| Rok vydání: | 2012 |
| Předmět: |
medicine.medical_specialty
business.industry lcsh:Surgery Functional latissimus dorsi flap long-term growth 030208 emergency & critical care medicine lcsh:RD1-811 030230 surgery Pulmonary compliance Jarcho–Levin syndrome Surgery body regions Vertebral body 03 medical and health sciences 0302 clinical medicine medicine Rib defects Breathing Original Article Respiratory system Latissimus dorsi flap business Jarcho-Levin syndrome Paradoxical respiration |
| Zdroj: | Indian Journal of Plastic Surgery : Official Publication of the Association of Plastic Surgeons of India Indian Journal of Plastic Surgery, Vol 45, Iss 01, Pp 040-044 (2012) |
| ISSN: | 1998-376X 0970-0358 |
| Popis: | Introduction: Jarcho-Levin syndrome is manifested by vertebral body and rib malformations. Large rib defects with paradoxical chest motion lead to early deathdue to progressive respiratory insufficiency, hence it is a lethal syndrome. The only means of improving survival is early stabilisation of the chest wall defect by containing the thoracic herniation. Nitcher et al. and Thatte et al. showed that reconstruction of the chest wall was life saving. Thatte et al. had postulated that early coverage of the lungs and thoracic contents with functional latissimus dorsi may prevent the visceral overgrowth and secondary pleural changes. Materials and Methods: Our three cases which had medium- and long-term follow-up help to support this postulation. Three patients were assessed retrospectively. Their ages at surgery were 6 months, 8 months and 1 year, respectively. All had laboured breathing and paradoxical respiration. All of them were operated with ipsilateral latissimus dorsi flap. Results: The results were evaluated clinically. The patients had reduced or no respiratory infections. The lung compliance improved and they had no tachypnoea on walking, running or playing. Conclusion: Hence, this can be used as a life-saving procedure for Jarcho-Levin syndrome on a long-term basis. |
| Databáze: | OpenAIRE |
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