The long-term survival in primary retroperitoneal mucinous cystadenocarcinoma: a case report
Autor: | Masahiro Ito, Ken Taniguchi, Naomi Matsumura, Yasuhiro Nagata, Hirotaka Tokai, Amane Kitasato, Tamotsu Kuroki, Shigeto Maeda, Hiroaki Takeshita, Hikaru Fujioka, Takayuki Tokunaga |
---|---|
Jazyk: | angličtina |
Rok vydání: | 2017 |
Předmět: |
medicine.medical_specialty
Right ovarian cyst 030219 obstetrics & reproductive medicine business.industry Uterine fibroids medicine.medical_treatment Cystadenocarcinoma lcsh:Surgery Case Report Retroperitoneal lcsh:RD1-811 medicine.disease Surgery 03 medical and health sciences Retroperitoneal tumor 0302 clinical medicine 030220 oncology & carcinogenesis Laparotomy Long term survival medicine Etiology Mucinous Mucinous cystadenocarcinoma business |
Zdroj: | Surgical Case Reports, Vol 3, Iss 1, Pp 1-7 (2017) Surgical Case Reports |
ISSN: | 2198-7793 |
DOI: | 10.1186/s40792-017-0394-z |
Popis: | Background Primary retroperitoneal mucinous cystadenocarcinoma (PRMC) is extremely rare, and its biological behavior, pathogenesis, optimum treatments, and prognosis remain to be elucidated. We herein report a case of PRMC with an 80-month follow-up. Case presentation A 29-year-old woman was diagnosed with unknown retroperitoneal tumor with benign right ovarian cyst and uterine fibroids, and she underwent laparotomy. The tumor was completely resected with a subsequent histopathological diagnosis of primary retroperitoneal mucinous cystadenocarcinoma (PRMC). Eighty months after surgery, she remains recurrence-free. Conclusion PRMC is an extremely rare tumor. Only around 60 cases have so far been published in the literature. The preoperative diagnosis of PRMC is difficult, and a definitive diagnosis can usually only be made based on the findings of histopathological examinations after surgery. Presently, only radical resection is useful for both diagnostic and therapeutic purposes. The optimal long-term management after surgery is still not well established. Further studies on PRMC are therefore needed to elucidate the etiology and establish effective treatments. |
Databáze: | OpenAIRE |
Externí odkaz: |