Vanishing gastroschisis visualized by antenatal ultrasound: a case report and review of literature

Autor: Corinne Hubinont, Milagros Marin Ponce, Catherine de Magnée, Dominique Hermans, Jean-Marc Biard
Přispěvatelé: UCL - SSS/IREC - Institut de recherche expérimentale et clinique, UCL - SSS/IREC/CHEX - Pôle de chirgurgie expérimentale et transplantation, UCL - (SLuc) Service d'obstétrique, UCL - (SLuc) Service de pédiatrie générale, UCL - (SLuc) Service de chirurgie et transplantation abdominale
Jazyk: angličtina
Rok vydání: 2018
Předmět:
Zdroj: European Journal of Obstetrics & Gynecology and Reproductive Biology, Vol. 228, no.(2018), p. 186-190 (2018)
Popis: We report a case of vanishing gastroschisis visualized by antenatal ultrasound with a 7-year long term follow-up. Currently, the child is still dependent on daily parenteral nutrition with no signs of hepatotoxicity. To our knowledge, it's the fourth case with a long-term follow-up. Vanishing gastroschisis is a rare complication of gastroschisis. However, physicians should be aware of it because its prognosis is worse than classical gastroschisis. When a vanishing gastroschisis is visualized or suspected by antenatal ultrasound, prenatal counseling is required with explanations about the risk of short bowel syndrome, the need of parenteral nutrition and related complications (inflammatory colitis, sepsis, liver failure and organ transplant). Mortality rate was initially around 93%, and dropped to 27% after the years 2000 (versus 10% for classical gastroschisis). After birth, all children will require surgery, and sometimes autologous gastro-intestinal reconstruction. Most survivors (68%) could be taken off the TPN. Unfortunately, long-term outcomes for children with vanishing gastroschisis are still missing in current literature.
Databáze: OpenAIRE