Spinal Cord Compression in Homozygous Beta-Thalassemia Intermedia
| Autor: | S. Toscano, E. Cardia, Domenico D'Avella, Francesco Tomasello, C. Zaccone, G. La Rosa |
|---|---|
| Rok vydání: | 1994 |
| Předmět: |
Pathology
medicine.medical_specialty Adolescent Central nervous system disease Bone Marrow Spinal cord compression medicine Humans Blood Transfusion business.industry beta-Thalassemia Hematopoietic Tissue Laminectomy Beta thalassemia General Medicine medicine.disease Spinal cord Magnetic Resonance Imaging Extramedullary hematopoiesis Hemoglobinopathy medicine.anatomical_structure Hematocrit Pediatrics Perinatology and Child Health Female Surgery Neurology (clinical) Tomography X-Ray Computed business Complication Spinal Cord Compression |
| Zdroj: | Pediatric Neurosurgery. 20:186-189 |
| ISSN: | 1423-0305 1016-2291 |
| DOI: | 10.1159/000120785 |
| Popis: | Symptomatic spinal cord compression caused by an epidural mass of extramedullary hematopoietic tissue in patients with beta-thalassemia is a rare occurrence, that becomes exceptional in childhood and adolescence. The literature is not uniform about the optimal treatment of these patients and different modes of therapy have been proposed so far, including surgical excision or decompressing laminectomy followed by local irradiation and/or hypertransfusional regimens. We report the successful treatment of such a complication in an adolescent with homozygous beta-thalassemia by surgery followed by repeated blood transfusions aimed at maintaining hematocrit at normal levels. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
|