Hunter's syndrome and associated sleep apnoea cured by CPAP and surgery
Autor: | D Veale, N Pinel, O. Orliaguet, Jean-Louis Pépin, Patrick Levy, E. Kelkel |
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Rok vydání: | 1999 |
Předmět: |
Pulmonary and Respiratory Medicine
Adult Male medicine.medical_specialty medicine.medical_treatment Positive pressure Vocal Cords Positive-Pressure Respiration Sleep Apnea Syndromes medicine Humans Continuous positive airway pressure Laryngeal Neoplasms Mucopolysaccharidosis II Sleep disorder business.industry Respiratory disease Myxoma Hunter syndrome medicine.disease nervous system diseases respiratory tract diseases Surgery Respiratory failure Anesthesia Airway business |
Zdroj: | The European respiratory journal. 13(5) |
ISSN: | 0903-1936 |
Popis: | A 42-yr-old male with Hunter's syndrome presented with severe obstructive sleep apnoea syndrome (OSAS) and daytime respiratory failure. Continuous positive airway pressure (CPAP) therapy was initially ineffective and produced acute respiratory distress. Extensive Hunter's disease infiltration of the upper airway with a myxoma was confirmed. Following surgery to remove the myxoma at the level of the vocal cords, CPAP therapy was highly effective and well tolerated. This report demonstrates the necessity of evaluating fully the upper airway in patients with unusual variants of OSAS, particularly where the disease is not adequately controlled by CPAP. |
Databáze: | OpenAIRE |
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