Upper Airway Function in Ondine's Curse

Autor: Terry S. Olson, Gayle E. Woodson, Gregory P. Heldt
Rok vydání: 1992
Předmět:
Zdroj: Archives of Otolaryngology - Head and Neck Surgery. 118:310-312
ISSN: 0886-4470
DOI: 10.1001/archotol.1992.01880030098020
Popis: • Congenital central alveolar hypoventilation (Ondine's curse) is a rare disorder with absence of automatic control of ventilation but preservation of voluntary breathing. Phrenic pacing, used to treat this condition, is usually not successful without a tracheotomy. We performed fiberoptic videoendoscopy on an affected infant airway. During wakefulness and ventilation by a negative pressure ventilator, the airway was normal, but with sleep onset, passive inspiration produced phasic epiglottic collapse. This case demonstrates the importance of central control in maintaining upper airway patency. ( Arch Otolaryngol Head Neck Surg. 1992;118:310-312)
Databáze: OpenAIRE