Vertebrobasilar dolichoectasia associated with Marfan syndrome
| Autor: | Robert J. Wityk, Gretchen L. Dike, Isaac E. Silverman, Gene Sung, Brian Litt, David M. Berman |
|---|---|
| Rok vydání: | 2000 |
| Předmět: |
Marfan syndrome
Aorta medicine.medical_specialty Subarachnoid hemorrhage business.industry Rehabilitation Autopsy Internal elastic lamina medicine.disease nervous system diseases Surgery Vertebrobasilar Dolichoectasia Myelopathy Ectasia medicine.artery cardiovascular system Medicine cardiovascular diseases Neurology (clinical) Cardiology and Cardiovascular Medicine business |
| Zdroj: | Journal of Stroke and Cerebrovascular Diseases. 9:196-198 |
| ISSN: | 1052-3057 |
| DOI: | 10.1053/jscd.2000.7224 |
| Popis: | We report a 37-year-old woman with Marfan syndrome (MFS) who presented with acute myelopathy secondary to a subdural spinal hematoma. The patient died of a subarachnoid hemorrhage 4 days later. Autopsy showed a markedly ectatic vertebrobasilar system with fragmentation of the internal elastic lamina. Microscopic examination of the aorta similarly showed a fragmented internal elastic lamina. We discuss the implications of our patient's early onset vertebrobasilar dolichoectasia; this intracranial disease represents a rare cause of subarachnoid hemorrhage in MFS. |
| Databáze: | OpenAIRE |
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