Patologia do bloqueio atrioventricular na cardiomiopatia por depósito de desmina

Autor: Breno de Alencar Araripe Falcão, Vera Dermarchi Aiello, Luiz Alberto Benvenuti, Silvia G. Lage
Jazyk: angličtina
Rok vydání: 2012
Předmět:
Zdroj: Arquivos Brasileiros de Cardiologia, Vol 98, Iss 1, Pp e3-e6 (2012)
Repositório Institucional da USP (Biblioteca Digital da Produção Intelectual)
Universidade de São Paulo (USP)
instacron:USP
ISSN: 1678-4170
Popis: Generally, restrictive cardiomyopathy due to desmin deposition is characterized by restriction to ventricular diastolic filling and different degrees of atrioventricular block (AVB). In this report, we describe the pathological changes of the cardiac conduction system related to AVB. The sinus node, the compact node, and the penetrating bundle (bundle of His) had no abnormalities, however, there was extensive fibrosis of the terminal portions of the branching bundle and the beginning of the left and right bundles at the top of the ventricular septum. The pathogenesis of this fibrous replacement is probably the same that leads to extensive fibrosis of the working ventricular myocardium, and remains to be elucidated.
Databáze: OpenAIRE