Portal vein thrombosis after splenectomy for hereditary stomatocytosis in childhood

Autor: Y. Perel, R. Barbier, M. Micheau, A Carrere, Jean-François Chateil, Bondonny Jm, D Dhermy
Rok vydání: 1999
Předmět:
Zdroj: European Journal of Pediatrics. 158:628-630
ISSN: 1432-1076
0340-6199
DOI: 10.1007/s004310051165
Popis: Portal vein thrombosis is a rare but potentially lethal complication in children requiring splenectomy. We report on a 15-year-old boy with a dehydrated hereditary stomatocytosis, who underwent splenectomy and presented a postoperative partial portal vein thrombosis. With prompt heparin therapy, neither propagation of the thrombus nor further cavernous transformation in the following occurred 6 years.Recent data suggest that hereditary stomatocytosis carries a high risk of thrombotic complications, especially after splenectomy. This procedure, the benefit of which is limited in this condition, should therefore be strongly avoided.
Databáze: OpenAIRE