Gastrointestinal Autonomic Nerve Sarcoma Presenting as a Giant Intra-Abdominal Cyst

Autor: Paul Mansour, James D. Evans, Anita Brown, David R. Jones
Rok vydání: 2000
Předmět:
Zdroj: Digestive Surgery. 17:407-410
ISSN: 1421-9883
0253-4886
DOI: 10.1159/000018889
Popis: Gastrointestinal autonomic nerve sarcomas are rare tumours. A 36-year-old man presented with abdominal pain, distension and constipation. Abdominal ultrasound and CT scanning demonstrated a giant cystic intra-abdominal mass. Laparotomy confirmed a large cystic mass arising from the ileum with multiple metastases. Immunohistochemical staining was positive for vimentin, neuronal-specific enolase and PGP9.5. This is the first reported case to present as a giant intra-abdominal cyst. Specialist histopathological and immunohistochemical analysis is essential to establish the diagnosis of this rare tumour.
Databáze: OpenAIRE