Primary pulmonary rhabdomyosarcoma arising within cystic adenomatoid malformation: a case report and review of the literature
| Autor: | Ahmet Çelik, Gulsen Kandiloglu, Zeliha Ural, E. Balik, Ali Veral, Coşkun Özcan |
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| Rok vydání: | 2001 |
| Předmět: |
Male
medicine.medical_specialty Lung Lung Neoplasms business.industry Respiratory disease Infant General Medicine medicine.disease Surgery medicine.anatomical_structure Cystic adenomatoid malformation Cystic Adenomatoid Malformation of Lung Congenital Pediatrics Perinatology and Child Health Rhabdomyosarcoma medicine Recurrent disease Congenital Cystic Adenomatoid Malformation Humans Histopathology Sarcoma business |
| Zdroj: | Journal of pediatric surgery. 36(7) |
| ISSN: | 0022-3468 |
| Popis: | The current report describes a 13-month-old boy with primary pulmonary rhabdomyosarcoma (RMS) that originated within a congenital cystic adenomatoid malformation (CCAM). To the best of our knowledge, he is the youngest patient of all primary pulmonary RMS cases reported in the English-language literature. The tumor, localized in left upper lobe, was removed completely, and histologic examination showed embryonal subtype. Postoperative systemic chemotherapy was carried out. Recent evaluation 15 months after resection has not identified any residual or recurrent disease. Primary pulmonary RMS, although very rare in the pediatric age group, should be considered in young patients with solitary pulmonary masses and associated cystic lesions. |
| Databáze: | OpenAIRE |
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