Adult Hirschsprung’s disease presenting as sigmoid volvulus: a case report and review of literature
| Autor: | F. L. S. Tan, S. M. Heah, Y.-M. Tan, F. Seow-Choen |
|---|---|
| Rok vydání: | 2006 |
| Předmět: |
Adult
Male medicine.medical_specialty medicine.medical_treatment digestive system Gastroenterology Ileostomy Internal medicine parasitic diseases medicine Humans Hirschsprung Disease Hirschsprung's disease Chronic constipation Sigmoid Diseases Megacolon medicine.diagnostic_test business.industry Proctocolectomy Megarectum Sigmoid colon Sigmoidoscopy medicine.disease digestive system diseases Surgery Radiography medicine.anatomical_structure business Intestinal Volvulus |
| Zdroj: | Techniques in Coloproctology. 10:245-248 |
| ISSN: | 1128-045X 1123-6337 |
| Popis: | Sigmoid volvulus is a rare presentation of Hirschsprung's disease. A 38-year-old male presented with acute intestinal obstruction and a history of chronic constipation since childhood. Abdominal radiographs showed megarectum and megacolon with dissipated feces. Sigmoidoscopy revealed gangrenous bowel mucosa affecting the sigmoid colon. Emergency laparotomy revealed a grossly dilated bowel with concurrent gangrenous sigmoid volvulus. He was treated successfully with proctocolectomy with J-pouch-anal anastomosis and a defunctioning ileostomy. Histological analysis was consistent with short segment Hirschsprung's disease. Although uncommon, adult Hirschsprung's disease is a cause of chronic constipation and can present acutely with a sigmoid volvulus. Mortality in cases with sigmoid volvulus is greater than in cases without (15.4% vs. 0%). A better awareness of this condition will facilitate management. |
| Databáze: | OpenAIRE |
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