Two Enlarged Kidneys: A Manifestation of Erdheim-Chester Disease
| Autor: | J.C. Piette, N. Costes Chalret, B. Wechsler, Olivier Aumaître, J. Ponsonnaille, Marc André, I. Delèvaux, B. de Fraissinette |
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| Rok vydání: | 2001 |
| Předmět: |
Male
Pathology medicine.medical_specialty Histiocytosis Non-Langerhans-Cell Heart disease business.industry macromolecular substances Middle Aged Kidney medicine.disease Nephropathy Histiocytosis Pericarditis medicine.anatomical_structure Nephrology Erdheim–Chester disease medicine Humans Abdomen Kidney Diseases Bone Diseases Enlarged kidney business Kidney disease |
| Zdroj: | American Journal of Nephrology. 21:315-317 |
| ISSN: | 1421-9670 0250-8095 |
| DOI: | 10.1159/000046267 |
| Popis: | Erdheim-Chester disease is a rare form of non-Langerhans’ cell histiocytosis. This disorder is characterized by a bone involvement and several extraskeletal manifestations. We describe the case of a patient with a pleural and pericardial effusion leading to tamponade. Pathological examination of pericardium and mediastinal adenopathy was normal. The abdominal computed tomography scan showed two enlarged kidneys suggestive of Erdheim-Chester disease. Bone scan scintigraphy demonstrated symmetrical increased labeling of the long bones. The biopsy of perirenal soft tissue confirmed the diagnosis of Erdheim-Chester disease. |
| Databáze: | OpenAIRE |
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