Isolated cerebral Rosai–Dorfman disease presenting as a sole mass protruding into the fourth ventricle: A case report
Autor: | Mathilde Duchesne, François Labrousse, Guillaume Friconnet, Aymeric Rouchaud, François Caire, Charbel Mounayer, Jean-François Emile, Marcel Gueye |
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Rok vydání: | 2021 |
Předmět: |
medicine.medical_specialty
R895-920 Case Report Fourth ventricle Cerebral Ventricles 030218 nuclear medicine & medical imaging Rosai–Dorfman Disease Meningioma Medical physics. Medical radiology. Nuclear medicine 03 medical and health sciences Posterior fossa 0302 clinical medicine Medicine Radiology Nuclear Medicine and imaging Pathological Rosai–Dorfman disease medicine.diagnostic_test business.industry Magnetic resonance imaging medicine.disease Magnetic Resonance Imaging Histiocytosis medicine.anatomical_structure Cerebellar peduncle Cerebral ventricle Radiology business 030217 neurology & neurosurgery |
Zdroj: | Radiology Case Reports, Vol 16, Iss 7, Pp 1613-1617 (2021) |
ISSN: | 1930-0433 |
DOI: | 10.1016/j.radcr.2021.04.021 |
Popis: | Rosai–Dorfman disease is a non–Langherans cell histiocytosis typically revealed by a lymphadenopathy. Central nervous system involvement is rare, exceptionally isolated, and usually consists of dural masses mimicking meningioma. Very few reports have described non-dural-based lesions, especially with an intra-ventricular development. We report hereby the case of a Rosai–Dorfman disease in a 30-year-old man presenting as an isolated mass arising from the right cerebellar peduncle and protruding into the fourth ventricle. We provide the results of the MRI examination with a special focus on advanced MRI features. As the diagnosis relies on pathological examination, we also detail the results of the analysis that followed the surgical resection of the mass including the immunohistochemical profile. This report highlights the necessity to consider Rosai–Dorfman disease as a potential diagnosis in case of an infra–tentorial mass and/or intra-ventricular mass. |
Databáze: | OpenAIRE |
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