Improved Quality of Life for Children With Beckwith–Wiedemann Syndrome Following Tongue Reduction Surgery
| Autor: | Tadashi Yamanishi, Juntaro Nishio, Takayuki Kurimoto, Takeshi Harada |
|---|---|
| Rok vydání: | 2019 |
| Předmět: |
Male
Thorax medicine.medical_specialty Beckwith-Wiedemann Syndrome Beckwith–Wiedemann syndrome 03 medical and health sciences 0302 clinical medicine Tongue Quality of life Enuresis medicine Macroglossia Humans Early childhood 030223 otorhinolaryngology business.industry 030206 dentistry General Medicine Airway obstruction medicine.disease Surgery Otorhinolaryngology Child Preschool Quality of Life Tongue reduction medicine.symptom business |
| Zdroj: | Journal of Craniofacial Surgery. 30:163-166 |
| ISSN: | 1049-2275 |
| DOI: | 10.1097/scs.0000000000004823 |
| Popis: | Macroglossia is observed in the majority of patients with Beckwith-Wiedemann syndrome (BWS), a congenital condition with characteristic anomalies. In addition, sleep disordered breathing (SDB) associated with macroglossia has occasionally been noted in BWS patients, for which tongue reduction surgery is generally performed. However, macroglossia is related to various health problems, such as eating and articulation disorders, attention deficit disorder, enuresis, and thorax deformation, as well as aesthetic issues. Therefore, in addition to treating airway obstruction, tongue reduction surgery can also exert favorable effects on the overall quality of life (QOL) of patients. However, surgical indications for tongue reduction have yet to be established and reports on QOL assessments after surgery are rare. The OSA-18 questionnaire is used for screening SDB and is also useful for assessing the effect of tongue reduction surgery on QOL. We report a patient whose QOL was improved by tongue reduction surgery. On the basis of our patient's results, we recommend tongue reduction surgery in early childhood not only to treat SDB but also to improve QOL. |
| Databáze: | OpenAIRE |
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