IgA nephritis in a patient with Alagille syndrome and a transplanted liver

Autor: Nisan Gilboa, Laszlo Hopp, Rocco M. Agostini
Rok vydání: 1992
Předmět:
Zdroj: Pediatric Nephrology. 6:559-561
ISSN: 1432-198X
0931-041X
DOI: 10.1007/bf00866506
Popis: Alagille syndrome (arteriohepatic dysplasia) is a major cause of intrahepatic cholestasis in infancy. The present report describes a patient with Alagille syndrome who presented with hematuria and IgA nephritis 7 years after an orthotopic liver transplantation and immunosuppression. This patient suggests that glomerular lipidosis is not an inherent feature of the Alagille syndrome, and that IgA nephritis may develop in spite of ongoing immunosuppressive treatment.
Databáze: OpenAIRE