Congenital pulmonary arteriovenous malformation: a rare cause of cyanosis in childhood
| Autor: | Hadi Kahrom, Hassan Mottaghi, Mahdi Kahrom, Mohammad Hassan Nezafati |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2010 |
| Předmět: |
Male
Pediatrics medicine.medical_specialty Population Pulmonary Artery Pulmonary arteriovenous malformation Arteriovenous Malformations Internal medicine Case report medicine Humans Medical journal Child education Cyanosis lcsh:R5-920 education.field_of_study business.industry lcsh:Public aspects of medicine Incidence (epidemiology) Congenital pulmonary arteriovenous malformation Infant Right to left shunting lcsh:RA1-1270 General Medicine Late childhood Shunting Adult life Pulmonary Veins Cardiology Pulmonary arteriovenous malformation Cyanosis Right to left shunting Female Differential diagnosis Gradual increase lcsh:Medicine (General) business |
| Zdroj: | Pan African Medical Journal; Vol 3, No 1 (2009) The Pan African Medical Journal, Vol 3, Iss 12 (2009) The Pan African medical journal |
| ISSN: | 1937-8688 |
| Popis: | Pulmonary arteriovenous malformations (PAVMs) are caused by abnormal communications between pulmonary arteries and pulmonary veins, which are most commonly congenital in nature. Although these lesions are uncommon, they are an important part of the differential diagnosis of common pulmonary problems such as hypoxaemia, pulmonary nodules and cyanosis. PAVM is a rare disorder with an incidence of 2-3 per 1,000,000 population. It occurs twice as often in women as in men, but there is a male predominance in newborns. Around 10% cases of PAVM are identified in infancy or childhood, followed by a gradual increase in the incidence through the fifth and sixth decades. Approximately 70% of the cases of PAVM are associated with hereditary haemorrhagic telangiectasia (HHT). Conversely, about 15 to 35% of patients with HHT have PAVM. PAVMs may cause hypoxaemia and dyspnoea due to right to left shunting, but frequently remain undiagnosed. This intrapulmonary malformation is described in two patients who presented with severe cyanosis. Index words: pulmonary arteriovenous malformation; cyanosis; right to left shunting DOI: 10.4038/cmj.v55i1.1707 Ceylon Medical Journal Vol.55, No.1 March 2010 pp.23-25 |
| Databáze: | OpenAIRE |
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