Craniofacial linear scleroderma associated with retinal telangiectasia and exudative retinal detachment

Autor: Eva Lenassi, Grace Vassallo, Jane Ashworth, Elias Kehdi, S. E Alice Chieng
Rok vydání: 2017
Předmět:
Male
medicine.medical_specialty
Fundus (eye)
Methylprednisolone
Scleroderma
Scleroderma
Localized

03 medical and health sciences
0302 clinical medicine
Ophthalmology
medicine
Humans
Linear Scleroderma
Enzyme Inhibitors
Fluorescein Angiography
Craniofacial
skin and connective tissue diseases
Glucocorticoids
integumentary system
medicine.diagnostic_test
business.industry
Retinal Detachment
Exudates and Transudates
Anatomy
Exudative retinal detachment
Mycophenolic Acid
medicine.disease
Fluorescein angiography
Magnetic Resonance Imaging
Retinal telangiectasia
Methotrexate
Scalp Dermatoses
Child
Preschool

Pediatrics
Perinatology and Child Health

030221 ophthalmology & optometry
Retinal Telangiectasis
Drug Therapy
Combination

En coup de sabre
business
Facial Dermatoses
Immunosuppressive Agents
030217 neurology & neurosurgery
Zdroj: Journal of American Association for Pediatric Ophthalmology and Strabismus. 21:251-254
ISSN: 1091-8531
DOI: 10.1016/j.jaapos.2016.12.004
Popis: Linear scleroderma is a characteristic form of scleroderma that typically affects children. Ocular manifestations may be present, especially when the frontoparietal area of the head is affected. We present the case of a 5-year-old boy with craniofacial linear scleroderma ("en coup de sabre") who developed exudative retinal detachment. Angiographic and neuroimaging findings are presented, and the importance of regular fundus examination is highlighted.
Databáze: OpenAIRE