Erdheim–Chester disease presenting as malignant exophthalmos
| Autor: | I. Rozenberg, G. Coscas, Y. Raulo, J. Hazard, Y. Pinaudeau, D. Larde, B. Brun, J. Wechsler, F. Koenig |
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| Rok vydání: | 1986 |
| Předmět: |
Male
medicine.medical_specialty Visual acuity Exophthalmos Eye disease Physical examination Lipidoses medicine Humans Radiology Nuclear Medicine and imaging Medical history Exophthalmus Radionuclide Imaging medicine.diagnostic_test biology business.industry General Medicine Middle Aged medicine.disease biology.organism_classification Dermatology Surgery Erdheim–Chester disease Histopathology medicine.symptom Tomography X-Ray Computed business |
| Zdroj: | The British Journal of Radiology. 59:173-177 |
| ISSN: | 1748-880X 0007-1285 |
| DOI: | 10.1259/0007-1285-59-698-173 |
| Popis: | In 1930, Chester working with Erdheim described a lipidosis which he distinguished from other lipogranulomatoses (Chester, 1931). Jaffe (1972) reported a similar case which he called “Erdheim–Chester disease”. Since then, few observations have been published. We report a further case of Erdheim–Chester disease presenting with bilateral proptosis. Clinical examination was completed by immunological tests, orbital and body CT, bone scan, and histopathology with electron microscopy. The course of the disease was slowed by treatment during a two-year period. A 57-year-old Caucasian man was admitted because of bilateral proptosis with recent and sudden diminution of visual acuity in the right eye. Exophthalmos had been noted three years earlier and the patient had been treated with prednisone. The proptosis was fluctuating. There was no previous medical history, except for mild untreated hypertension. He had gained 4 kg in weight over the previous three years. There were no skeletal symptoms. |
| Databáze: | OpenAIRE |
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