Carney's Complex with Primary Pigmented Nodular Adrenocortical Disease and Spotty Pigmentations

Autor: Ichiro Komiya, Noriko Ohara, Teiji Takeda, Hiromi Ohtsuka, Nobuyuki Takasu, Yoshitaka Nagasawa, Keishi Yamauchi
Rok vydání: 1993
Předmět:
Zdroj: Internal Medicine. 32:60-62
ISSN: 1349-7235
0918-2918
Popis: Carney's complex is composed of myxoma, spotty pigmentation and endocrine overactivity. A 27-year-old male was diagnosed to have Carney's complex on the basis of intense spotty pigmentations on his face, soles and palms, and bilateral adrenal nodular hyperplasia on computed tomography scanning (CT) and magnetic resonance imaging (MRI). Total bilateral adrenectomy was done; histological findings were compatible with primary pigmented adrenocortical disease (PPNAD). Recently, his sister and one of his brothers were suspected to have Carney's complex with PPNAD. We report the first familial case of Carney's complex with PPNAD and spotty pigmentations in Japan.
Databáze: OpenAIRE