Spontaneous pneumothorax as manifestation of Marfan syndrome
Autor: | Patricia Rocha, Cristiana Carvalho, Maria Manuel Zarcos, Carolina Viveiro |
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Rok vydání: | 2013 |
Předmět: |
Marfan syndrome
Male medicine.medical_specialty Adolescent medicine.medical_treatment Physical examination Article Marfan Syndrome Mitral valve medicine Humans medicine.diagnostic_test business.industry Thoracic Surgery Video-Assisted Pneumothorax General Medicine Marfanoid habitus medicine.disease Surgery respiratory tract diseases Respiratory Medicine medicine.anatomical_structure surgical procedures operative Cardiothoracic surgery business Pleurodesis |
Zdroj: | BMJ case reports. 2013 |
ISSN: | 1757-790X |
Popis: | The authors describe a 16-year-old boy, previously healthy, who was admitted to our hospital for left-sided spontaneous pneumothorax. On physical examination he presented with marfanoid habitus. Pneumothorax was managed conservatively with resolution. Four months later he had a recurrence of left-sided pneumothorax and 1 week after that he presented with contralateral pneumothorax. He underwent video-assisted thoracoscopic surgery twice for bullectomy and pleurodesis. No further recurrence was stated. Additional investigation showed a prolapsed cardiac mitral valve and Marfan syndrome was confirmed genetically. |
Databáze: | OpenAIRE |
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