Open abdominal aortic aneurysm repair with incidental finding of an extra-adrenal pheochromocytoma of the organ of Zuckerkandl
Autor: | Michael J. Singh, Kathy Gonzalez |
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Jazyk: | angličtina |
Rok vydání: | 2020 |
Předmět: |
Pathology
medicine.medical_specialty endocrine system business.industry Extra-Adrenal 030209 endocrinology & metabolism General Medicine Neuroendocrine tumors medicine.disease Abdominal aortic aneurysm Article Pheochromocytoma 03 medical and health sciences 0302 clinical medicine medicine.anatomical_structure Paraganglioma 030220 oncology & carcinogenesis medicine cardiovascular system Radiology Nuclear Medicine and imaging Surgery Cardiology and Cardiovascular Medicine Adrenal medulla Organ of Zuckerkandl business |
Zdroj: | Vascular |
Popis: | Objectives Pheochromocytomas are rare catecholamine-secreting neuroendocrine tumors that arise from chromaffin cells of the adrenal medulla or extra-adrenal paraganglia. The most common location of these tumors is within the adrenal medulla. Extra-adrenal pheochromocytomas (EAPs) may occur in any portion of the paraganglion system. The most common location of EAPs is at the organ of Zuckerkandl, which is a collection of chromaffin cells near the origin of the inferior mesenteric artery. Methods We present a case of an EAP of the organ of Zuckerkandl incidentally discovered and resected during urgent open repair of a symptomatic 6.7-cm juxtarenal abdominal aortic aneurysm (AAA). Results The patient underwent successful open surgical repair of a juxtarenal AAA and resection of the pheochromocytoma. Conclusions Concomitant pheochromocytomas and abdominal aortic aneurysms are rare, with a small number described in the literature. We describe the case of a simultaneous EAP of the organ of Zuckerkandl and AAA repair. This case demonstrates that these lesions can be safely resected in the same setting as AAA repair. |
Databáze: | OpenAIRE |
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