Primary granulocytic sarcoma in the sphenoidal bone and orbit
| Autor: | Yoshiyuki Kohsaka, Eiji Kohmura, Kohei Ohta, Kensaku Yasuo, Takeshi Kondoh |
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| Rok vydání: | 2003 |
| Předmět: |
Male
medicine.medical_specialty Visual acuity Exophthalmos medicine.medical_treatment Sphenoid bone Visual Acuity Drug Therapy Sphenoid Bone medicine Humans Myeloid Cells Sarcoma Myeloid Craniotomy medicine.diagnostic_test business.industry Brain Neoplasms Remission Induction Magnetic resonance imaging General Medicine Abducens palsy medicine.disease Magnetic Resonance Imaging Surgery Review Literature as Topic medicine.anatomical_structure Child Preschool Pediatrics Perinatology and Child Health Neurology (clinical) Sarcoma medicine.symptom business Tomography X-Ray Computed Orbit Carotid Artery Internal Orbit (anatomy) |
| Zdroj: | Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery. 19(9) |
| ISSN: | 0256-7040 |
| Popis: | We report a case of a primary cranial chloroma in boy aged 2 years and 8 months. The symptoms were progressive bilateral exophthalmos, right abducens palsy, and bilateral papilledema. The tumor was partially calcified and was a round mass located in the bilateral sphenoidal bone extending into the orbit. Laboratory study did not show hematological abnormality. The tumor was partially removed by bilateral frontotemporal craniotomy and a diagnosis of primary granulocytic sarcoma was made from the surgical specimen. Progressive deterioration of visual acuity was seen and chemotherapy started on the 11th postoperative day followed by local cranium irradiation (24 Gy). The patient has been in complete remission for 37 months. The visual acuity recovered partially and follow-up magnetic resonance imaging showed a significant decrease in the size of the tumor.Radiological diagnosis of primary intracranial granulocytic sarcoma is difficult. Surgical removal may be an option for progressive neurological deterioration but chemotherapy is more important for both neurological stabilization and induction of remission. |
| Databáze: | OpenAIRE |
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