The orthopaedic management of long bone deformities in genetically and acquired generalized bone weakening conditions
| Autor: | T. Wirth |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2019 |
| Předmět: |
Orthodontics
030222 orthopedics business.industry Fibrous dysplasia Long bone fibrous dysplasia Bone deformity osteogenesis imperfecta Hypophosphataemic rickets medicine.disease hypophosphataemic rickets bone deformity 03 medical and health sciences 0302 clinical medicine medicine.anatomical_structure Osteogenesis imperfecta Pediatrics Perinatology and Child Health Long bone deformity medicine Orthopedics and Sports Medicine 030212 general & internal medicine business Current Concepts Review |
| Zdroj: | Journal of Children's Orthopaedics |
| ISSN: | 1863-2548 1863-2521 |
| Popis: | Purpose Diseases such as osteogenesis imperfecta, fibrous dysplasia, hypophosphataemic rickets and others lead to soft and weak bones and long bone deformity in affected patients. As a consequence, these patients lose their walking capacity and functional abilities of the upper extremities as well. Methods In combination with bisphosphonate treatment and physical rehabilitation programmes surgical interventions are being applied to correct and stabilize the deformed and less mechanically resistant long bones. Intramedullary devices, ideally with an elongating telescopic mechanism, have proven to be the most suitable implants. Results The surgical correction and stabilization of deformed bones in weak bone diseases is very beneficial to the patients. Pain restriction, reduction of fracture events, minimization of consequences of traumatic events and falls have resulted in a significant functional improvement. The patients live on a better activity level with a much-improved individual independence. Despite a high complication and revision rate of the intramedullary rods the gain of quality of life outweighs these negative aspects by far. Conclusion Orthopaedic surgical treatment for deformed bones in patients with weak bone diseases has changed the life of the patients and plays a very important role in the disease management protocols. This paper was written under the guidance of the Study Group Genetics and Metabolic Diseases of the European Paediatric Orthopaedic Society. |
| Databáze: | OpenAIRE |
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