Clinical Characteristics and Follow-Up of Pediatric-Onset Arrhythmogenic Right Ventricular Cardiomyopathy
| Autor: | Robert W. Roudijk, Lisa Verheul, Laurens P. Bosman, Mimount Bourfiss, Johannes M.P.J. Breur, Martijn G. Slieker, Andreas C. Blank, Dennis Dooijes, Jeroen F. van der Heijden, Freek van den Heuvel, Sally-Ann Clur, Floris E.A. Udink ten Cate, Maarten P. van den Berg, Arthur A.M. Wilde, Folkert W. Asselbergs, J. Peter van Tintelen, Anneline S.J.M. te Riele |
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| Přispěvatelé: | Paediatric Cardiology, ACS - Amsterdam Cardiovascular Sciences, Cardiology, ACS - Heart failure & arrhythmias, Cardiovascular Centre (CVC), Nephrology, ACS - Atherosclerosis & ischemic syndromes, Pediatric surgery |
| Jazyk: | angličtina |
| Rok vydání: | 2022 |
| Předmět: |
Adult
Male Adolescent cascade screening Vascular damage Radboud Institute for Health Sciences [Radboudumc 16] heart failure CHILDREN DIAGNOSIS pediatric-onset sudden cardiac death Electrocardiography Young Adult TASK-FORCE CRITERIA All institutes and research themes of the Radboud University Medical Center AGE ADOLESCENTS Humans genetics Child Arrhythmogenic Right Ventricular Dysplasia RISK arrhythmogenic right ventricular cardiomyopathy Arrhythmias Cardiac Heart Arrest Death Sudden Cardiac Tachycardia Ventricular ventricular tachycardia Follow-Up Studies |
| Zdroj: | Roudijk, R W, Verheul, L, Bosman, L P, Bourfiss, M, Breur, J M P J, Slieker, M G, Blank, A C, Dooijes, D, van der Heijden, J F, van den Heuvel, F, Clur, S-A, Udink ten Cate, F E A, van den Berg, M P, Wilde, A A M, Asselbergs, F W, Peter van Tintelen, J & te Riele, A S J M 2022, ' Clinical Characteristics and Follow-Up of Pediatric-Onset Arrhythmogenic Right Ventricular Cardiomyopathy ', JACC: Clinical Electrophysiology, vol. 8, no. 3, pp. 306-318 . https://doi.org/10.1016/j.jacep.2021.09.001 JACC: Clinical Electrophysiology, 8(3), 306-318. Elsevier USA JACC. Clinical electrophysiology, 8(3), 306-318. Elsevier JACC. Clinical Electrophysiology, 8, 306-318 JACC. Clinical Electrophysiology, 8, 3, pp. 306-318 |
| ISSN: | 2405-500X |
| DOI: | 10.1016/j.jacep.2021.09.001 |
| Popis: | Objectives: The goal of this study was to describe characteristics, cascade screening results, and predictors of adverse outcome in pediatric-onset arrhythmogenic right ventricular cardiomyopathy (ARVC). Background: Although ARVC is increasingly recognized in children, pediatric ARVC cohorts remain underrepresented in the literature. Methods: This study included 12 probands with pediatric-onset ARVC (aged 1-V 3 (P < 0.01), premature ventricular complexes/runs (P ≤ 0.01), and decrease in biventricular ejection fraction (P ≤ 0.01) were associated with VT occurrence. Conclusions: Pediatric ARVC carries high arrhythmic risk, especially in probands. Disease progression is particularly observed on electrocardiogram or Holter monitoring. Arrhythmic events are associated with male sex, T-wave inversions, premature ventricular complexes/runs, and reduced biventricular ejection fraction. |
| Databáze: | OpenAIRE |
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