The management of pediatric hearing loss caused by auditory neuropathy spectrum disorder
| Autor: | Nguyen S. Pham |
|---|---|
| Rok vydání: | 2017 |
| Předmět: |
medicine.medical_specialty
Speech perception Hearing loss Audiology 03 medical and health sciences 0302 clinical medicine Speech discrimination Auditory neuropathy spectrum disorder otorhinolaryngologic diseases medicine Evoked Potentials Auditory Brain Stem Vestibulocochlear Nerve Diseases Humans Spectrum disorder Hearing Loss Central 030223 otorhinolaryngology Child Cochlea business.industry medicine.disease Cochlear Implantation Normal otoacoustic emissions Cochlear Implants Otorhinolaryngology Speech Perception Surgery Brainstem medicine.symptom business 030217 neurology & neurosurgery |
| Zdroj: | Current opinion in otolaryngologyhead and neck surgery. 25(5) |
| ISSN: | 1531-6998 |
| Popis: | Auditory neuropathy spectrum disorder (ANSD) is a condition in which auditory testing reveals normal otoacoustic emissions, but auditory brainstem testing is abnormal or absent and speech discrimination is poor. This constellation of findings ostensibly suggests that the cochlea is healthy and an abnormality of conduction or processing of sound occurs along the nerve fibers. As more is learned about this condition, it is becoming clear that ANSD describes heterogeneous, distinct clinical entities that must be taken into account when devising treatment modalities.Modern auditory testing, genetic testing, and neuroimaging can allow for an accurate understanding of the location of the lesion causing ANSD in the auditory pathway. Contributing causes can include genetic mutations, absent or deficient cochlear nerve, hypoxia and jaundice among others. Hearing aids can be successful in the management of ANSD. Several studies suggest that cochlear implantation can lead to successful hearing outcomes in a subset of this patient population.Auditory neuropathy spectrum disorder represents a relatively rare but important diagnosis for clinicians. Treatment for this condition includes hearing aids and FM systems in more mild cases, and cochlear implants in severe cases. Cochlear implantation for many patients can lead to a good hearing outcomes but the outcome can vary greatly depending on the underlying etiology of ANSD. |
| Databáze: | OpenAIRE |
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