Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature
| Autor: | Elif Güler, Mine Genc, Kamil Karaali, Gülen Tüysüz, Alper Tunga Derin, Koray Yalcin, Irem Hicran Ozbudak, Alphan Kupesiz |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2020 |
| Předmět: |
Adult
Male medicine.medical_specialty tonsillar neoplasm dysphagia medicine.medical_treatment Tonsillar Neoplasms synovial sarcoma Palatine tonsil Pathology and Forensic Medicine Sarcoma Synovial stomatognathic system medicine Parapharyngeal space otorhinolaryngologic diseases lcsh:Pathology Humans pediatric tumor Chemotherapy business.industry respiratory system medicine.disease Dysphagia Synovial sarcoma Tonsillectomy Radiation therapy Treatment Outcome medicine.anatomical_structure Radiology medicine.symptom Positive Surgical Margin Deglutition Disorders business snoring lcsh:RB1-214 |
| Zdroj: | Türk Patoloji Dergisi, Vol 36, Iss 1, Pp 082-086 (2020) |
| ISSN: | 1309-5730 1018-5615 |
| Popis: | Tonsillar synovial sarcoma is an extremely rare entity and only 9 adult patients have been reported up to now. Here, we describe the first pediatric tonsillar synovial sarcoma of the literature in a patient who presented with a 2-month history of dysphagia and snoring. Clinical and radiological examinations showed that the tumor arose from the right palatine tonsil and narrowed the parapharyngeal space. An incisional biopsy from the palatine tonsil revealed the diagnosis of synovial sarcoma. The patient has underwent total tonsillectomy and received radiotherapy and chemotherapy because of the positive surgical margins. The patient is clinically in good condition and free of tumor 30 months after the initial diagnosis. We achieved a long-term complete remission with a combination of surgery, radiotherapy and chemotherapy in our case. Tonsillar synovial sarcoma should be kept in mind while dealing with tonsillar masses. We can conclude that a multidisciplinary approach is warranted while treating synovial sarcoma with this localization. |
| Databáze: | OpenAIRE |
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