Giant Terminal Myelocystocele: A Case Report
| Autor: | Deepak Gupta, Gaurav Varshney |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2020 |
| Předmět: |
medicine.diagnostic_test
Spina bifida business.industry Spinal dysraphism General Neuroscience Rare entity Magnetic resonance imaging Case Report Anatomy medicine.disease Lumbosacral region Lumbosacral mass Terminal (electronics) terminal myelocystocele Pediatrics Perinatology and Child Health medicine spinal dysraphism business Myelocystocele Lumbosacral joint |
| Zdroj: | Journal of Pediatric Neurosciences |
| ISSN: | 1998-3948 1817-1745 |
| Popis: | Myelocystoceles, also known as syringoceles, syringomyeloceles, and lipomeningomyelocystoceles, represent 5% of all lumbosacral skin-covered masses. Terminal myelocystocele (TMC) is a rare variant of spinal dysraphism. At times, patients with TMCs can present with a huge lumbosacral mass (giant TMC). A 14-month-old female child presented with progressive increasing swelling in the lumbosacral region (35 cm × 35 cm × 30 cm) since birth with inability to move both lower limbs. Magnetic resonance imaging revealed a dilated terminal central canal herniating through a spina bifida defect (from L4 to S2) into a huge meningocele, suggestive of a giant TMC. The girl was operated on successfully and was doing well at 6 months follow-up, although neurologically unchanged. Giant TMC is a rare entity and only a few case reports are available in literature. Herein we present a case with TMC with the largest dimensions reported till date. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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