Pierre-Marie-Bamberger syndrome and solitary fibrous tumor: a rare association
| Autor: | Estefanía Boyer-Duck, Luis Ángel Hernández-Arenas, Marco Polo Macías-Morales, Adriana Rodríguez-Gómez, Catalina Romo-Aguirre, Walid Leonardo Dajer-Fadel |
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| Rok vydání: | 2018 |
| Předmět: |
Adult
Image-Guided Biopsy Pulmonary and Respiratory Medicine Pathology medicine.medical_specialty Solitary fibrous tumor Paraneoplastic Syndromes 03 medical and health sciences 0302 clinical medicine Spinal osteoarthropathy medicine Humans 030203 arthritis & rheumatology business.industry Osteoarthropathy Secondary Hypertrophic Soft tissue General Medicine Fibrous Tumor medicine.disease Immunohistochemistry Hypertrophic osteoarthropathy Bronchogenic carcinoma Solitary Fibrous Tumor Pleural Treatment Outcome Positron-Emission Tomography 030220 oncology & carcinogenesis Female Surgery Tomography X-Ray Computed Cardiology and Cardiovascular Medicine business Bone surface Calcification |
| Zdroj: | Asian Cardiovascular and Thoracic Annals. 26:154-157 |
| ISSN: | 1816-5370 0218-4923 |
| DOI: | 10.1177/0218492318757042 |
| Popis: | A solitary fibrous tumor originates in the pleura with variable degrees of invasion. Hypertrophic osteoarthropathy, known as Pierre-Marie-Bamberger syndrome, is characterized by clubbing of the fingers due to bone surface and soft tissue calcification, historically known as a bronchogenic carcinoma paraneoplastic syndrome; however, a few cases have been associated with solitary fibrous tumors. We describe the case of a 38-year-old woman who presented with clubbing of the fingers. Studies revealed an intrathoracic fibrous tumor that was successfully treated with improvement in symptoms. |
| Databáze: | OpenAIRE |
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