Dental Manifestations of Ehlers-Danlos Syndromes: A Systematic Review
| Autor: | F. M. Pope, Johannes Zschocke, Schnabl D, Ines Kapferer-Seebacher |
|---|---|
| Rok vydání: | 2020 |
| Předmět: |
Joint hypermobility
medicine.medical_specialty Dentinogenesis imperfecta 0206 medical engineering 02 engineering and technology Dermatology 03 medical and health sciences 0302 clinical medicine stomatognathic system lcsh:Dermatology medicine Humans Tooth Root ehlers-danlos syndromes business.industry Tooth Abnormalities oral manifestation Overlap syndrome 030206 dentistry General Medicine dental anomaly lcsh:RL1-803 medicine.disease 020601 biomedical engineering Hypoplasia Ehlers danlos stomatognathic diseases hypermobility Osteogenesis imperfecta Tooth Diseases Pulp (tooth) Dental Pulp Calcification Ehlers-Danlos Syndrome business Calcification |
| Zdroj: | Acta Dermato-Venereologica, Vol 100, Iss 7, p adv00092 (2020) |
| ISSN: | 1651-2057 |
| Popis: | Ehlers-Danlos syndromes (EDS) are a group of inherited connective tissue disorders characterized by joint hypermobility, skin hyperextensibility, and variable tissue fragility. However, there are limited published data on the dental manifestations of EDS. This review systematically assessed the spectrum of published dental anomalies in various types of EDS. Twenty-four individual case reports/series and 3 longer case-control studies, reporting on a total of 84 individuals with a clinical diagnosis of EDS, were included in the data analysis. The main dental features listed in classical EDS were pulp calcification and localized root hypoplasia. Common dental abnormalities observed in vascular EDS were pulp shape modifications (52.2%), exceeding root length (34.8%), and molar root fusion (47.8%). Dentinogenesis imperfecta is a consistent finding in osteogenesis imperfecta/EDS overlap syndrome. Data on dental manifestations in other types of EDS are both rare and generally inconclusive. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
|