Tetralogy of Fallot with severe ascending aortic enlargement in early childhood

Autor:	Satoshi Okugi, Masaaki Koide, Yoshifumi Kunii, Minori Tateishi, Risa Shimbori, Hiroki Moriuchi, Yoshiro Otsuki
Rok vydání:	2021
Předmět:	Pulmonary and Respiratory Medicine Arterial Switch Operation Heart Defects Congenital Pulmonary Atresia Child Preschool Tetralogy of Fallot Humans Surgery Female General Medicine Hypertrophy Cardiology and Cardiovascular Medicine Aorta
Zdroj:	General thoracic and cardiovascular surgery. 70(5)
ISSN:	1863-6713
Popis:	The Rastelli procedure is indicated for repair of tetralogy of Fallot (TOF) with pulmonary atresia. However, currently, there are no criteria available for concomitant surgical intervention for an enlarged ascending aorta in infancy. We report a rare case of TOF with pulmonary atresia complicated by severe enlargement of the ascending aorta in a girl aged 2 years and 5 months. We performed the Rastelli procedure with ascending aorta replacement. Pathological findings of the ascending aorta included fragmentation of elastic fibers and loss of smooth muscle cells. Postoperatively, the patient remained healthy and asymptomatic. This case indicates that ascending aortic enlargement in conotruncal anomalies may be associated with pathological lesion even in early childhood. Replacement of the diseased aorta could be considered as a concomitant procedure with definitive repair for conotruncal anomalies presenting with severe ascending aortic enlargement.
Databáze:	OpenAIRE
Externí odkaz:	https://explore.openaire.eu/search/publication?articleId=doi_dedup___::57dd6c2bfa04404b45497adce1db8984 https://pubmed.ncbi.nlm.nih.gov/35098488 Zobrazit plný text záznamu Full text from SpringerLink