Delayed Presentation of a Congenital Cholesteatoma in a 64-year-old Man: Case Report and Review of the Literature
| Autor: | Nishant Hemanth Davidoss, Rupan Banga, Gunesh P. Rajan, Jennifer F. Ha |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2014 |
| Předmět: |
medicine.medical_specialty
Hearing loss review lcsh:Surgery Asymptomatic Article lcsh:RC346-429 massive Temporal bone medicine otorhinolaryngologic diseases cholesteatoma lcsh:Neurology. Diseases of the nervous system large hearing loss Foramen magnum business.industry mastoid Occipital bone congenital Postoperative complication Cholesteatoma Epidermoid cyst incidental lcsh:RD1-811 medicine.disease Surgery medicine.anatomical_structure Neurology (clinical) medicine.symptom business management |
| Zdroj: | Journal of Neurological Surgery Reports, Vol 75, Iss 01, Pp e113-e116 (2014) Journal of Neurological Surgery Reports |
| ISSN: | 2193-6366 2193-6358 |
| Popis: | Introduction Congenital cholesteatomas of the temporal bone are epidermoid cysts of embryologic origin that result in progressive desquamation and trapping of squamous epithelium behind an intact tympanic membrane. They are benign, slowly progressive lesions that can be found in various areas of the temporal bone. We report a case of a patient with a massive cholesteatoma first detected at the age of 64 years, causing significant destruction of the mastoid and petrous temporal bones, and adjacent occipital bone. Methods We reviewed the literature and a case report of a patient seen in our institution recently. The Medline database was used to search multiple terms including “congenital” and “cholesteatoma.” Results The patient's congenital cholesteatoma was detected incidentally on a computed tomography scan when the patient's only symptoms were unilateral conductive hearing loss with a family history of hearing loss. It was subsequently successfully operated on with minimal postoperative complications. Conclusions Congenital cholesteatomas of mastoid origin can often exist for many years in a subclinical state and develop into a massive size before causing symptoms. A high index of suspicion is necessary to detect congenital cholesteatomas in patients with unilateral conductive hearing loss who are otherwise asymptomatic and have a normal tympanic membrane. |
| Databáze: | OpenAIRE |
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