ANTI-MA2 encephalitis mimicking diencephalic demyelinating syndrome

Autor: Orlando Graziani Povoas Barsottini, Agábio Diógenes Pessoa Neto, Lívia Almeida Dutra, Rodrigo Alencar e Silva, Bárbara Cristina Vieira de Aquino, Paulo Santiago de Morais Brito, Manuel Moreira Neto, Clécio de Oliveira Godeiro Junior
Jazyk: angličtina
Rok vydání: 2021
Předmět:
Zdroj: Interdisciplinary Neurosurgery, Vol 23, Iss, Pp 100980-(2021)
ISSN: 2214-7519
Popis: Anti Ma 2 encephalitis is an autoimmune encephalitis, usually paraneoplastic, characterized by isolated or combined limbic, diencephalic, or brainstem dysfunction. Limbic encephalitis (LE) is the most common manifestation. Anti-Ma2 LE can also be manifested as a pure psychiatric disturbance associated or not with hypokinesia. Other patients exhibit excessive daytime sleepiness, vertical ophthalmoparesis, or both associated with LE, due to diencephalic and/or upper brainstem involvement. These cases are challenging and demand extensive work-up for differential diagnosis.
Databáze: OpenAIRE