ANTI-MA2 encephalitis mimicking diencephalic demyelinating syndrome
Autor: | Orlando Graziani Povoas Barsottini, Agábio Diógenes Pessoa Neto, Lívia Almeida Dutra, Rodrigo Alencar e Silva, Bárbara Cristina Vieira de Aquino, Paulo Santiago de Morais Brito, Manuel Moreira Neto, Clécio de Oliveira Godeiro Junior |
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Jazyk: | angličtina |
Rok vydání: | 2021 |
Předmět: |
Pathology
medicine.medical_specialty lcsh:Surgery Excessive daytime sleepiness Autoimmunity lcsh:RC346-429 030218 nuclear medicine & medical imaging Ophthalmoparesis 03 medical and health sciences 0302 clinical medicine Hypokinesia medicine lcsh:Neurology. Diseases of the nervous system Autoimmune encephalitis business.industry Limbic encephalitis lcsh:RD1-811 medicine.disease Paraneoplastic encephalitis Surgery Neurology (clinical) Brainstem Differential diagnosis medicine.symptom Diencephalic lesion business 030217 neurology & neurosurgery Encephalitis |
Zdroj: | Interdisciplinary Neurosurgery, Vol 23, Iss, Pp 100980-(2021) |
ISSN: | 2214-7519 |
Popis: | Anti Ma 2 encephalitis is an autoimmune encephalitis, usually paraneoplastic, characterized by isolated or combined limbic, diencephalic, or brainstem dysfunction. Limbic encephalitis (LE) is the most common manifestation. Anti-Ma2 LE can also be manifested as a pure psychiatric disturbance associated or not with hypokinesia. Other patients exhibit excessive daytime sleepiness, vertical ophthalmoparesis, or both associated with LE, due to diencephalic and/or upper brainstem involvement. These cases are challenging and demand extensive work-up for differential diagnosis. |
Databáze: | OpenAIRE |
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