Malignant presentation of uterine lymphangioleiomyomatosis
| Autor: | Rafał Moszyński, Pawel Zielinski, Sebastian Szubert, Andrzej Frankowski, Dariusz Szpurek, Stefan Sajdak |
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| Rok vydání: | 2015 |
| Předmět: |
Pathology
medicine.medical_specialty Lung Neoplasms Angiomyolipoma Ovariectomy medicine.medical_treatment lymphangioleiomyomatosis tuberous sclerosis Hysterectomy lcsh:Gynecology and obstetrics Metastasis Diagnosis Differential Ovarian tumor Obstetrics and Gynaecology medicine Humans metastasis Uterine Neoplasm lcsh:RG1-991 Retrospective Studies Laparotomy uterus business.industry Obstetrics and Gynecology Middle Aged medicine.disease genital track Leiomyoma Uterine Neoplasms Lymphangioleiomyomatosis Female Differential diagnosis Tomography X-Ray Computed business |
| Zdroj: | Taiwanese Journal of Obstetrics & Gynecology, Vol 54, Iss 5, Pp 603-607 (2015) |
| ISSN: | 1028-4559 |
| DOI: | 10.1016/j.tjog.2015.08.015 |
| Popis: | Objective The main aim of this case report was to present the method of diagnosis, management, and the 12-year-follow-up of a patient diagnosed with primary uterine lymphangioleiomyomatosis (LAM). Case Report A 47-year-old woman was admitted to the Department of Thoracosurgery due to pulmonary lesions suspected to be metastatic. The potential primary site of the neoplasm was not identified by previous imaging studies and specialist counseling. The patient had a history of total abdominal hysterectomy without ovaries due to a uterine tumor recognized as cellular leiomyoma and left salpingo-oophorectomy due to a solid ovarian tumor also recognized as leiomyoma. She had previously undergone the removal of a left kidney angiomyolipoma. After histopathological examination of the pulmonary lesions and repeated evaluation of the ovarian and uterine tumors, the diagnosis of primary uterine LAM with metastases to the ovary and the lungs was established. Although new metastatic lesions occurred, the patient remained in good condition during the 12-year-follow-up. Conclusion The history of our patient and review of the literature suggest that although uterine LAM presents malignant features (i.e., metastasis), the disease is long lasting and the patient can be in good condition for a number of years. |
| Databáze: | OpenAIRE |
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