Incontinentia pigmenti (Bloch-Sulzberger syndrome) manifesting as painful periungual and subungual tumours
| Autor: | R. D. G. Peachey, P. L. G. Townsend, A. Adeniran |
|---|---|
| Rok vydání: | 1993 |
| Předmět: |
Adult
Transplantation Pathology medicine.medical_specialty business.industry Genodermatosis Incontinentia pigmenti medicine.disease Skin Diseases Chronic paronychia 03 medical and health sciences Keratoacanthoma 0302 clinical medicine Nails 030225 pediatrics Bloch-Sulzberger syndrome Medicine Humans Surgery Female sense organs Incontinentia Pigmenti skin and connective tissue diseases Previously treated business |
| Zdroj: | Journal of hand surgery (Edinburgh, Scotland). 18(5) |
| ISSN: | 0266-7681 |
| Popis: | A 25-year-old lady presented with painful periungual tumours which were associated with lytic changes of underlying terminal phalanges. She had been previously treated as a case of chronic paronychia but the problem recurred. She was subsequently diagnosed as a case of Incontinentia pigmenti which is a rare genodermatosis with mixed ectodermal and mesodermal polydysplasias, onchychodystrophy being a very rare manifestation. She was treated by excision of painful finger lesions, but there is no specific treatment for the underlying condition. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
|