PRIMARY TRACHEOBRONCHIAL AMYLOIDOSIS: A SERIES OF 3 CASES
| Autor: | B. Dieriks, Marc Meysman, Shane Hanon, L. Vanmaele, T. De Keukeleire, Walter Vincken, W. Bultynck, Marc Noppen |
|---|---|
| Rok vydání: | 2007 |
| Předmět: |
Adult
Male medicine.medical_specialty Biopsy Radiography Pulmonary function testing Diagnosis Differential Prosthesis Implantation Bronchoscopy medicine Humans Tracheal Diseases medicine.diagnostic_test business.industry Amyloidosis Bronchial Diseases General Medicine Middle Aged Prognosis Debulking medicine.disease Surgery Tracheobronchial amyloidosis Radiological weapon Female Radiography Thoracic Stents Tomography X-Ray Computed business |
| Zdroj: | Acta Clinica Belgica. 62:56-60 |
| ISSN: | 2295-3337 1784-3286 |
| DOI: | 10.1179/acb.2007.009 |
| Popis: | Primary tracheobronchial amyloidosis is a form of localized pulmonary amyloidosis, characterised by the deposition of AL-amyloid in trachea and bronchi. It is a rare and slowly progressive disease, usually requiring repeated endoscopic treatment. In this case series we describe symptoms, diagnostic and therapeutic procedures, radiological findings and pulmonary function testing in 3 cases of different presentation and severity. Two patients were treated by endoscopic debulking and stent placement during rigid bronchoscopy, both with excellent clinical and functional results. In one of these patients regular endoscopic and clinical control exams were performed in the 5 years following the initial treatment, showing stable disease, requiring no further therapeutic intervention until today. |
| Databáze: | OpenAIRE |
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