Short-term outcome after the prenatal diagnosis of right aortic arch

Autor: Bo B. Bet, Maartje C. Snoep, Elisabeth van Leeuwen, Ingeborg H. Linskens, Monique C. Haak, Lieke Rozendaal, Ingmar Knobbe, Joost van Schuppen, Carlijn E. L. Hoekstra, David R. Koolbergen, Sally‐Ann Clur, Eva Pajkrt
Přispěvatelé: Graduate School, Obstetrics and Gynaecology, Amsterdam Reproduction & Development (AR&D), Radiology and Nuclear Medicine, Ear, Nose and Throat, Cardiothoracic Surgery, ACS - Heart failure & arrhythmias, Paediatric Cardiology, Amsterdam Cardiovascular Sciences, APH - Personalized Medicine, APH - Quality of Care, Obstetrics and gynaecology, Pediatrics
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: Bet, B B, Snoep, M C, van Leeuwen, E, Linskens, I H, Haak, M C, Rozendaal, L, Knobbe, I, van Schuppen, J, Hoekstra, C E L, Koolbergen, D R, Clur, S-A & Pajkrt, E 2023, ' Short-term outcome after the prenatal diagnosis of right aortic arch ', Prenatal Diagnosis, vol. 43, no. 5, pp. 629-638 . https://doi.org/10.1002/pd.6326
Prenatal diagnosis. John Wiley and Sons Ltd
Prenatal Diagnosis, 43(5), 629-638. John Wiley and Sons Ltd
ISSN: 0197-3851
Popis: Objectives: To determine the proportion of children that require surgery in the first year of life and thereafter in order to improve the counseling of parents with a fetus with a right aortic arch (RAA). Methods: Fetuses diagnosed with isolated RAA, defined as the absence of intra- or extracardiac anomalies, between 2007 and 2021 were extracted from the prospective registry PRECOR. Results: In total, 110 fetuses were included, 92 with a prenatal diagnosis of RAA and 18 with double aortic arch (DAA). The prevalence of 22q11 deletion syndrome was 5.5%. Six pregnancies were terminated and five cases were false-positive; therefore, the follow-up consisted of 99 neonates. Surgery was performed in 10 infants (10%) in the first year of life. In total, 25 (25%) children had surgery at a mean age of 17 months. Eight of these 25 (32%) had a DAA. Only one child, with a DAA, required surgery in the first week of life due to obstructive stridor. Conclusions: Children with a prenatally diagnosed RAA are at a low risk of acute respiratory postnatal problems. Delivery in a hospital with neonatal intensive care and pediatric cardiothoracic facilities seems only indicated in cases with suspected DAA. Expectant parents should be informed that presently 25% of the children need elective surgery and only incidentally due to acute respiratory distress.
Databáze: OpenAIRE
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