Erythrokeratodermia Variabilis with Erythema Gyratum Repens‐Like Lesions
| Autor: | Meirav Cohen-Bar-Dayan, Barukh Mevorah, Joseph Ophir, Charles R. Wolf, Marina Landau, Daniel Hohl, Andrea Gat |
|---|---|
| Rok vydání: | 2002 |
| Předmět: |
Adult
Male Heterozygote Erythema gyratum repens Pathology medicine.medical_specialty Congenital ichthyosiform erythroderma Hyperkeratosis Erythroderma Dermatology Severity of Illness Index Sampling Studies Erythrokeratodermia variabilis Humans Medicine Genetic Predisposition to Disease Netherton syndrome Israel Child Aged Hyperkeratosis Epidermolytic business.industry Biopsy Needle Infant Newborn Infant Skin Diseases Genetic Ichthyosiform Erythroderma Congenital Middle Aged Prognosis medicine.disease Immunohistochemistry Dyskeratosis Pedigree Malignant Atrophic Papulosis Erythema Pediatrics Perinatology and Child Health Female medicine.symptom business |
| Zdroj: | Pediatric Dermatology. 19:285-292 |
| ISSN: | 1525-1470 0736-8046 |
| DOI: | 10.1046/j.1525-1470.2002.00085.x |
| Popis: | A large pedigree with erythrokeratodermia variabilis (EKV) and erythema gyratum repens-like lesions is described. Clinical, laboratory, and histologic findings of this family are presented. The differential diagnoses of the following dermatoses with an erythematous and a hyperkeratotic component are discussed: erythrokeratodermia variabilis (Mendes da Costa), progressive symmetric erythrokeratoderma (Gottron), loricrin keratoderma, erythrokeratoderma en cocardes (Degos), Netherton syndrome, keratitis-ichthyosis-deafness (KID) syndrome, erythrokeratolysis hiemalis (Oudtshoorn disease), and nonbullous congenital ichthyosiform erythroderma. |
| Databáze: | OpenAIRE |
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