Tumor de Evans de la mano. Una localización excepcional
| Autor: | P. Gómez, J. F. Gutiérrez, J. A. Requena, J. A. Macia |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2007 |
| Předmět: |
Economics and Econometrics
Soft Tissue Neoplasm business.industry Mesenchymal Tumor lcsh:Surgery Forestry Intermediate signal intensity Myxoid stroma lcsh:RD1-811 medicine.disease sarcoma fibromixoide tumor evans Low-grade fibromyxoid sarcoma tumor mesenquimal Materials Chemistry Media Technology medicine Soft tissue mass Sarcoma Clinical case Nuclear medicine business sarcoma partes blandas |
| Zdroj: | Revista Iberoamericana de Cirugía de la Mano, Vol 35, Iss 01, Pp 043-047 (2007) |
| ISSN: | 1698-8396 |
| DOI: | 10.1055/s-0037-1606706 |
| Popis: | Introduccion. El sarcoma fibromixoide de bajo grado es un sarcoma de partes blandas caracterizado por un curso clinico y una histologia aparentemente benigna, pero que puede dar recidivas locales y metastasis a distancia. La cirugia constituye el tratamiento de eleccion. Caso clinico. Varon de 30 anos que presenta tumoracion indolora en eminencia tenar mano izquierda de 12 meses de evolucion. En la primera exploracion se aprecia un nodulo duro y fijo en region tenar izquierda, que en la resonancia magnetica con contraste se localizaba a la altura de la base del primer metacarpiano con captacion heterogenea de contraste. La puncion aspirativa con aguja fina es compatible con tumor mesenquimal, por lo que se opta por un tratamiento quirurgico de conformidad con el paciente. El estudio anatomopatologico definitivo establece el diagnostico de sarcoma fibromixoide de bajo grado sin infiltracion tumoral de los bordes quirurgicos y estudio de extension negativo. Al ano de control clinico, no existen indicios de recidiva tumoral, ni local ni a distancia. La presentacion superficial, en extremidades superiores o en edad pediatrica es excepcional. Introduction. Low-grade fibromyxoid sarcomas are uncommon deep soft tissue neoplasms first described by Evans in 1987. They exhibit a deceptively benign appearance, with a whorled or linear arrangement of spindle-shaped cells showing few to absent mitoses. A characteristic, but not specific, feature is the presence of areas of myxoid stroma. Recurrences are common, and late metastases have been recorded. Surgery is the election treatment. Clinical case. A 30-year-old man presented with a year history of a painless slow-growing mass in the left hand. In the first exploration a hard and fixed nodule is appraised in the left first metacarpal bone. Magnetic resonance images were obtained demonstrating a well defined mildly heterogeneous soft tissue mass of intermediate signal intensity. A pre-operative fine needle aspiration was a suspicion of mesenchymal tumor. The tumor was diagnosed as low grade fibromyxoid sarcoma. Immunohistochemistry was performed to confirm the diagnosis. The patient had no evidence of local recurrence or metastases after a year of follow-up. Low-grade fibromyxoid sarcoma (LGFMS), usually a deeply situated mass in adults, is uncommon in superficial soft tissue, upper extremities and in children. |
| Databáze: | OpenAIRE |
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