Sjogren-Larsson syndrome: a dermato-histopathological study
| Autor: | P.‐Å. Hofer, S. Jagell |
|---|---|
| Rok vydání: | 1982 |
| Předmět: |
Adult
Male Pathology medicine.medical_specialty Histology Adolescent Hyperkeratosis Acanthosis Dermatology Papillomatosis Pathology and Forensic Medicine Diagnosis Differential Intellectual Disability Humans Paralysis Medicine Child Parakeratosis Aged Skin Sjögren–Larsson syndrome integumentary system medicine.diagnostic_test business.industry Ichthyosis Infant Newborn Infant Keratosis Syndrome Cubital fossa Middle Aged medicine.disease medicine.anatomical_structure Muscle Spasticity Child Preschool Skin biopsy Female medicine.symptom business |
| Zdroj: | Journal of Cutaneous Pathology. 9:360-376 |
| ISSN: | 1600-0560 0303-6987 |
| DOI: | 10.1111/j.1600-0560.1982.tb01075.x |
| Popis: | Thirty-six Swedish patients with the recessively inherited Sjögren-Larsson syndrome (SLS) were examined by histopathologic and, in some cases, morphometric techniques. Skin biopsy specimens were taken on the volar side of the right forearm below the cubital fossa. The histopathological picture was characterized by a moderate to pronounced hyperkeratosis that could include follicular hyperkeratosis. The stratum granulosum was thickened. There was acanthosis and usually some papillomatosis. These observations were in accordance with the morphometric measurements. There was often a slight, chronic infiltrate in the upper dermis. The ichthyosis in SLS can be included in the recessively inherited, congenital group, with a seemingly lower tendency to parakeratosis. |
| Databáze: | OpenAIRE |
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