Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement
| Autor: | Karademir, Selmin, Keskin, Mahmut, Ozgur, Senem, Orun, Utku Arman, Dogan, Vehbi, Koc, Murat, Ceylan, Ozben, YILMAZ, OSMAN |
|---|---|
| Rok vydání: | 2014 |
| Předmět: |
Pulmonary and Respiratory Medicine
medicine.diagnostic_test business.industry medicine.medical_treatment Interrupted aortic arch Hasta medicine.disease medicine.anatomical_structure Ductus arteriosus Angiography medicine Surgery Persistent left superior vena cava Cardiology and Cardiovascular Medicine Nuclear medicine business Coronary sinus Cardiac catheterization Tetralogy of Fallot |
| Zdroj: | Turkish Journal of Thoracic and Cardiovascular Surgery. 22:7-12 |
| ISSN: | 1301-5680 |
| Popis: | Amac: Bu calismada koroner sinusu genis olan hastalarda buyuk torasik venlerin donus anormalliklerini saptayabilmede ekokardiyografinin rolu arastirildi. Calismaplani:Ocak 2010 Subat 2012 tarihleri arasinda klinigimizde alti hastaya (3 erkek, 3 kiz; ort. yas 4.1; dagilim 3 gun 9 yil) kalici sol superior vena kavanin (SVK) eslik ettigi sag superior vena kava (SVK) yoklugu tanisi konuldu. Sag SVC yoklugu tanisi ekokardiyografi ve anjiyografi ile konuldu. Bul gu lar: Dort hastada sag SVK yoklugu tanisi ekokardiyografi ile teyit edildi. Iki hastada ise, kardiyak kateterizasyon ve anjiyografi ile tani konuldu. Ek kardiyak anomaliler periferik pulmoner darlik, patent duktus arteriyozus, Fallot tetralojisi, atriyal septal defekt, ventrikuler septal defekt ve kesintili aortik ark tip B idi. Bir hasta Trizomi 9p sendromlu iken, digeri diyabetik bir annenin bebegi idi. Uc hasta klinik izleme alindi, diger uc hasta ameliyat edildi. Sonuc:Ekokardiyografi ile ortaya kondugu uzere, koroner sinusun genis oldugu, koroner sinus akiminin arttigi ve kalici sol SVK’nin goruldugu olgularda sag SVK yoklugunun dikkatli bir sekilde arastirilmasi gerekmektedir. Anah tar soz cuk ler: Sag superior vena kava yoklugu; dogustan kalp hastaligi; diyabetik anne bebegi; kalici sol superior vena kava; Trizomi 9p sendromu. Background: This study aims to investigate the role of echocardiography in the detection of venous anomalies of large thoracic veins in patients with large coronary sinus. Methods: Between January 2010 and March 2012, six patients (3 boys, 3 girls; mean age 4.1; range 3 days 9 years) were diagnosed with an absent right superior vena cava (RSVC) accompanied by persistent left superior vena cava (PLSVC) in our clinic. The diagnosis of the absent RSVC was established by echocardiography and angiography. Results:Diagnosis of the absent RSVC was confirmed by echocardiography in four patients. The diagnosis was based on cardiac catheterization and angiography in two patients. Additional cardiac anomalies included peripheral pulmonary stenosis, patent ductus arteriosus, tetralogy of Fallot, atrial septal defect, ventricular septal defect and interrupted aortic arch type B. One patient had Trisomy 9p syndrome, while another one was the baby of a diabetic mother. Three patients were followed clinically, while other three patients were operated. Conclusion: Absent RSVC should be thoroughly investigated in cases with a large coronary sinus along with increased coronary sinus flow and PLSVC, as evidenced by echocardiography. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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