Idiopathic retroperitoneal and mediastinal fibrosis mimicking connective tissue disease
| Autor: | Nader Morad, Sharon Eypper, Steven L. Strongwater, Bruce A. Woda |
|---|---|
| Rok vydání: | 1987 |
| Předmět: |
Pathology
medicine.medical_specialty Parietal Pericardium business.industry Respiratory disease Mediastinum Connective tissue Retroperitoneal Fibrosis General Medicine medicine.disease Fibrosis Connective tissue disease Scleroderma Diagnosis Differential Mediastinal fibrosis medicine.anatomical_structure medicine Humans Female medicine.symptom Connective Tissue Diseases business Aged |
| Zdroj: | The American Journal of Medicine. 82:363-366 |
| ISSN: | 0002-9343 |
| DOI: | 10.1016/0002-9343(87)90089-1 |
| Popis: | Combined retroperitoneal and mediastinal fibrosis is a rare manifestation of an idiopathic systemic sclerosing disease. This report describes a multisystem illness that clinically could best be described as polyserositis and progressive renal failure. Pathologically, it was characterized by diffuse infiltration of retroperitoneal and mediastinal tissues with plaquelike fibrofatty connective tissue encasing the kidneys, ureters, adrenal glands, and parietal pericardium. These features are diagnostic of a systemic sclerosing disease. It is important to recognize this unusual disorder to avoid confusion with other systemic connective tissue diseases such as systemic lupus erythematosus. |
| Databáze: | OpenAIRE |
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