Coexistence of nodular regenerative hyperplasia of the liver and pulmonary arterial hypertension in patients with connective tissue diseases: report of three cases and review of the literature

Autor: Tohru Akahoshi, Hirobumi Kondo, Jun Okada, Shigehiro Kokubu, Yuko Kurihara, Hiroyuki Watabe
Rok vydání: 2006
Předmět:
Zdroj: Modern Rheumatology. 16:389-394
ISSN: 1439-7609
1439-7595
DOI: 10.3109/s10165-006-0514-2
Popis: Nodular regenerative hyperplasia of the liver (NRH) is known to be a rare condition in patients with connective tissue diseases (CTD). In this report, we document three patients with CTD who had both NRH and pulmonary hypertension (PH). All three patients developed PH during their course and thereafter developed NRH. The clinical course of these patients suggests that circulatory disturbance caused by PH might be a trigger for NRH.
Databáze: OpenAIRE