Anesthetic Management of a Patient with Cri Du Chat Syndrome. Case Report
| Autor: | Ziltomar Donizetti de Oliveira Borges, Klaus Morales dos Santos, Daniel Câmara de Rezende |
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| Rok vydání: | 2010 |
| Předmět: |
Cri-du-Chat Syndrome
Male ANESTHESIA: ambulatorial Adolescent Sedation Cri du Chat Syndrome SEDAÇÃO ANESTESIA: ambulatorial Risk Factors Micrognathism medicine Humans Anesthesia Strabismus business.industry SEDATION medicine.disease Thyromental distance Anesthesiology and Pain Medicine DOENÇAS Genética: síndrome de Cri Du Chat Hypertonia Midazolam medicine.symptom Propofol business DISEASES Genetic: Cri Du Chat syndrome medicine.drug |
| Zdroj: | Brazilian Journal of Anesthesiology. 60(6):630-633 |
| ISSN: | 0034-7094 |
| DOI: | 10.1016/s0034-7094(10)70078-7 |
| Popis: | Background and objectives Cri Du Chat syndrome is a chromosomal disorder with peculiar clinical characteristics including airways abnormalities that require special care by anesthesiologists when handling those patients. Objective To present a case of outpatient anesthesia in a patient with Cri Du Chat syndrome and discuss the anesthetic aspects related to this disorder. Case report Male patient, 14 years old, 25 kg, with Cri Du Chat syndrome, physical status ASA P2, was admitted for upper gastrointestinal endoscopy and esophageal dilation. The patient had mental retardation, a few episodes of seizures, and marked hypertonia of the limbs. Airways exam showed limited cervical mobility and thyromental distance less than six centimeters. The patient was unable to comprehend verbal commands, making it difficult to undertake a complete assessment of the airways. Other findings on physical exam included microcephaly, micrognathism, subtle strabismus, limb hypertonia with flexion, and protrusion of the tip of the tongue. Intravenous fentanyl 50 μg, midazolam 1 mg, and propofol 60 mg were administered. The patient was maintained on spontaneous ventilation. The procedure lasted 5 minutes, without intercurrences. Conclusions Patients with Cri Du Chat syndrome have clinical characteristics that are very important for their anesthetic management, being the responsibility of the anesthesiologist to consider carefully the structural particularities of each patient. |
| Databáze: | OpenAIRE |
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