The congenital intrahepatic arterioportal fistula syndrome: elucidation and proposed classification
| Autor: | Justine M. Turner, Seamus P Norton, Stanley P Moroz, Vicky L. Ng, Philip John, Kevan Jacobson, Gordon Culham |
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| Rok vydání: | 2006 |
| Předmět: |
Male
medicine.medical_specialty Gastrointestinal bleeding medicine.medical_treatment Fistula Hepatic Artery Melena Hypertension Portal medicine Arterioportal fistula Humans Embolization Vascular disease business.industry Portal Vein Gastroenterology Infant medicine.disease Embolization Therapeutic Surgery Abdominal Pain Failure to Thrive Treatment Outcome Child Preschool Pediatrics Perinatology and Child Health Failure to thrive Arteriovenous Fistula Portal hypertension medicine.symptom business Tomography X-Ray Computed |
| Zdroj: | Journal of pediatric gastroenterology and nutrition. 43(2) |
| ISSN: | 0277-2116 |
| Popis: | Congenital intrahepatic arterioportal fistula is a rare but treatable cause of portal hypertension for which early recognition may lead to successful radiological management. We report an infant presenting with severe failure to thrive, melena and splenomegaly due to a congenital intrahepatic arterioportal fistula, successfully ablated after multiple trials of superselective transarterial embolization. Comprehensive review of congenital cases provides an understanding of the key clinical features defining this syndrome. A classification system is proposed, upon which treatment decisions may be based. |
| Databáze: | OpenAIRE |
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