Cochlear Implantation in Patients With Usher Syndrome Type IIa Increases Performance and Quality of Life
| Autor: | Wendy J. Huinck, Ronald J.E. Pennings, Liselotte J. C. Rotteveel, Josephine W. I. van Nierop, Bas P. Hartel, Emmanuel A. M. Mylanus, Ad F. M. Snik, Henricus P. M. Kunst |
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| Rok vydání: | 2017 |
| Předmět: |
Male
0301 basic medicine medicine.medical_specialty Speech perception Usher syndrome medicine.medical_treatment Sensory disorders Radboud Institute for Health Sciences [Radboudumc 12] Audiology Sensory disorders Donders Center for Medical Neuroscience [Radboudumc 12] 03 medical and health sciences 0302 clinical medicine Acquired immunodeficiency syndrome (AIDS) Quality of life Surveys and Questionnaires medicine otorhinolaryngologic diseases Humans Early childhood 030223 otorhinolaryngology Aged Retrospective Studies Rehabilitation business.industry Speech Intelligibility Case-control study Retrospective cohort study Middle Aged medicine.disease Cochlear Implantation Sensory Systems Treatment Outcome 030104 developmental biology Otorhinolaryngology Case-Control Studies Quality of Life Speech Perception Female Neurology (clinical) business Usher Syndromes Rare cancers Radboud Institute for Health Sciences [Radboudumc 9] |
| Zdroj: | Otology & Neurotology, 38, 6, pp. e120-e127 Otology & Neurotology, 38, e120-e127 |
| ISSN: | 1531-7129 |
| DOI: | 10.1097/mao.0000000000001441 |
| Popis: | Item does not contain fulltext OBJECTIVES: Usher syndrome type IIa (USH2a) is characterized by congenital moderate to severe hearing impairment and retinitis pigmentosa. Hearing rehabilitation starts in early childhood with the application of hearing aids. In some patients with USH2a, severe progression of hearing impairment leads to insufficient speech intelligibility with hearing aids and issues with adequate communication and safety. Cochlear implantation (CI) is the next step in rehabilitation of such patients. This study evaluates the performance and benefit of CI in patients with USH2a. DESIGN: Retrospective case-control study to evaluate the performance and benefit of CI in 16 postlingually deaf adults (eight patients with USH2a and eight matched controls). Performance and benefit were evaluated by a speech intelligibility test and three quality-of-life questionnaires. RESULTS: Patients with USH2a with a mean age of 59 years at implantation exhibited good performance after CI. The phoneme scores improved significantly from 41 to 87% in patients with USH2a (p = 0.02) and from 30 to 86% in the control group (p = 0.001). The results of the questionnaire survey demonstrated a clear benefit from CI. There were no differences in performance or benefit between patients with USH2a and control patients before and after CI. CONCLUSIONS: CI increases speech intelligibility and improves quality of life in patients with USH2a. |
| Databáze: | OpenAIRE |
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