Respiratory failure due to muscle weakness in inflammatory myopathies: maintenance therapy with home mechanical ventilation

Autor: T. Mijares‐Boeckh‐Behrens, J. Angel Bosch‐Gil, F. Morell‐Brotad, Miguel Vilardell‐Tarrés, Roser Solans-Laqué, Albert Selva-O'Callaghan, X. Muñoz‐Gall, L. Sanchez‐Sitjes
Rok vydání: 2000
Předmět:
Zdroj: Scopus-Elsevier
ISSN: 1462-0324
Popis: Polymyositis and dermatomyositis are idiopathic inflammatory myopathies. Respiratory complications are a common feature, but ventilatory insufficiency is rare in these patients. We describe here three patients diagnosed with inflammatory myopathy (polymyositis) with respiratory failure due to muscle weakness who did not respond to immunosuppressive therapy. Mechanical ventilation at home with nasal or tracheal intermittent positive pressure resulted in improved chronic hypoventilation. This treatment improves the quality of life of patients with inflammatory myopathies and can be lifesaving in some cases.
Databáze: OpenAIRE