Focal scleroderma in children: an orthopaedic perspective
| Autor: | R K Ashley, P James, S Skinner, S L Buckley |
|---|---|
| Rok vydání: | 1993 |
| Předmět: |
musculoskeletal diseases
Male medicine.medical_specialty Contracture Adolescent Disarticulation medicine.medical_treatment Artificial Limbs Scleroderma Localized Medicine Humans Orthopedics and Sports Medicine Linear Scleroderma Joint Contracture Child Muscle contracture Patient Care Team business.industry Epiphysiodesis Infant General Medicine medicine.disease Combined Modality Therapy Surgery Casts Surgical Joint Deformities Acquired medicine.anatomical_structure Child Preschool Pediatrics Perinatology and Child Health Upper limb Female medicine.symptom Ankle business |
| Zdroj: | Journal of pediatric orthopedics. 13(6) |
| ISSN: | 0271-6798 |
| Popis: | Focal scleroderma is a connective-tissue disorder manifested by fibrosis of the skin and subcutaneous tissues. Consequently, it may be associated with joint contractures, extremity deformity, and impairment of extremity function. It has a variable clinical course, with both remissions and recurrences. In resistant cases of extremity involvement, treatment considerations should include physical and occupational therapy, medical treatment, bracing, serial casting, and surgical intervention. We reviewed seven patients treated between 1960 and 1990 with significant joint contractures secondary to focal scleroderma. Serial casting was found to be useful for contractures about the wrist, knee, and ankle. Soft-tissue release was an effective treatment for contractures at the wrist, hip, and ankle. Knee disarticulation was performed on one patient with a severe knee-flexion contracture. Epiphysiodesis and femoral shortening osteotomy were effective treatments for leg-length equalization in a case of hemiatrophy. |
| Databáze: | OpenAIRE |
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